Acute Myopericarditis as the First Manifestation of Familial Mediterranean Fever: A Case Report Article Swipe
YOU?
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· 2024
· Open Access
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· DOI: https://doi.org/10.7759/cureus.54170
Familial Mediterranean fever (FMF) is an autoinflammatory disorder, characterized by recurrent episodes of fever and polyserositis, and usually presents during the first two decades of life. Acute pericarditis is a rare manifestation of FMF and typically presents with other symptoms of the inflammatory disorder. A 27-year-old Arabian male presented to our hospital with pleuritic chest pain and shortness of breath while lying flat. His electrocardiogram showed changes suggestive of pericarditis, and his inflammatory markers and troponin were raised. His echocardiogram revealed a moderate-sized pericardial effusion with septa and a normal left ventricular function. He had a strong family history of FMF and consanguinity of the parents. He was treated for acute myopericarditis with colchicine and ibuprofen, and his symptoms improved gradually along with his inflammatory markers and troponin. Six weeks after discharge, he had a cardiac MRI, which revealed a thickened pericardium with profound enhancement (features suggestive of pericarditis) and no signs of myocarditis. He was asymptomatic, and his markers and troponin were within the normal range. His colchicine medication was continued indefinitely, and he was referred to a tertiary care hospital with a specialized periodic fever clinic for follow-up and genotype testing.
Related Topics
- Type
- article
- Language
- en
- Landing Page
- https://doi.org/10.7759/cureus.54170
- https://assets.cureus.com/uploads/case_report/pdf/227759/20240214-31434-lhokhq.pdf
- OA Status
- diamond
- Cited By
- 1
- References
- 16
- Related Works
- 10
- OpenAlex ID
- https://openalex.org/W4391822405
Raw OpenAlex JSON
- OpenAlex ID
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https://openalex.org/W4391822405Canonical identifier for this work in OpenAlex
- DOI
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https://doi.org/10.7759/cureus.54170Digital Object Identifier
- Title
-
Acute Myopericarditis as the First Manifestation of Familial Mediterranean Fever: A Case ReportWork title
- Type
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articleOpenAlex work type
- Language
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enPrimary language
- Publication year
-
2024Year of publication
- Publication date
-
2024-02-14Full publication date if available
- Authors
-
Abdalla Khalil, Andrew D. Greenhalgh, Shovhit Gurung, Harmeet ChanaList of authors in order
- Landing page
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https://doi.org/10.7759/cureus.54170Publisher landing page
- PDF URL
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https://assets.cureus.com/uploads/case_report/pdf/227759/20240214-31434-lhokhq.pdfDirect link to full text PDF
- Open access
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YesWhether a free full text is available
- OA status
-
diamondOpen access status per OpenAlex
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https://assets.cureus.com/uploads/case_report/pdf/227759/20240214-31434-lhokhq.pdfDirect OA link when available
- Concepts
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Familial Mediterranean fever, Myopericarditis, Medicine, Pericarditis, Pericardial effusion, Colchicine, Acute pericarditis, Chest pain, Asymptomatic, Internal medicine, Serositis, Myocarditis, Cardiology, Troponin, Pediatrics, Myocardial infarction, DiseaseTop concepts (fields/topics) attached by OpenAlex
- Cited by
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1Total citation count in OpenAlex
- Citations by year (recent)
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2025: 1Per-year citation counts (last 5 years)
- References (count)
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16Number of works referenced by this work
- Related works (count)
-
10Other works algorithmically related by OpenAlex
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| primary_topic.display_name | Inflammasome and immune disorders |
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