Matrix metalloproteinase activity in the lung is increased in Hermansky-Pudlak syndrome Article Swipe
Ross Summer
,
R. Vijay Krishna
,
DeLeila Schriner
,
Karina Cuevas-Mora
,
Dominic Sales
,
Rachel Para
,
Jesse Roman
,
Carl Nieweld
,
Bernadette R. Gochuico
,
Freddy Romero
·
YOU?
·
· 2019
· Open Access
·
· DOI: https://doi.org/10.1186/s13023-019-1143-0
YOU?
·
· 2019
· Open Access
·
· DOI: https://doi.org/10.1186/s13023-019-1143-0
In summary, our findings indicate that MMP activity is dysregulated in the HPS lung, suggesting a role for these proteases as biological markers or pathogenic players in HPS lung disease.
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Metadata
- Type
- article
- Language
- en
- Landing Page
- https://doi.org/10.1186/s13023-019-1143-0
- https://ojrd.biomedcentral.com/track/pdf/10.1186/s13023-019-1143-0
- OA Status
- gold
- Cited By
- 21
- References
- 40
- Related Works
- 10
- OpenAlex ID
- https://openalex.org/W2955455335
All OpenAlex metadata
Raw OpenAlex JSON
- OpenAlex ID
-
https://openalex.org/W2955455335Canonical identifier for this work in OpenAlex
- DOI
-
https://doi.org/10.1186/s13023-019-1143-0Digital Object Identifier
- Title
-
Matrix metalloproteinase activity in the lung is increased in Hermansky-Pudlak syndromeWork title
- Type
-
articleOpenAlex work type
- Language
-
enPrimary language
- Publication year
-
2019Year of publication
- Publication date
-
2019-07-04Full publication date if available
- Authors
-
Ross Summer, R. Vijay Krishna, DeLeila Schriner, Karina Cuevas-Mora, Dominic Sales, Rachel Para, Jesse Roman, Carl Nieweld, Bernadette R. Gochuico, Freddy RomeroList of authors in order
- Landing page
-
https://doi.org/10.1186/s13023-019-1143-0Publisher landing page
- PDF URL
-
https://ojrd.biomedcentral.com/track/pdf/10.1186/s13023-019-1143-0Direct link to full text PDF
- Open access
-
YesWhether a free full text is available
- OA status
-
goldOpen access status per OpenAlex
- OA URL
-
https://ojrd.biomedcentral.com/track/pdf/10.1186/s13023-019-1143-0Direct OA link when available
- Concepts
-
Downregulation and upregulation, Lung, Hermansky–Pudlak syndrome, Pulmonary fibrosis, Matrix metalloproteinase, Biology, Pathology, Bronchoalveolar lavage, Idiopathic pulmonary fibrosis, Cancer research, Fibrosis, Medicine, Internal medicine, Gene, BiochemistryTop concepts (fields/topics) attached by OpenAlex
- Cited by
-
21Total citation count in OpenAlex
- Citations by year (recent)
-
2025: 2, 2024: 2, 2023: 3, 2022: 3, 2021: 7Per-year citation counts (last 5 years)
- References (count)
-
40Number of works referenced by this work
- Related works (count)
-
10Other works algorithmically related by OpenAlex
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