Maryam Piram
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View article: Pediatric trichodysplasia spinulosa in skin of color
Pediatric trichodysplasia spinulosa in skin of color Open
View article: Incidence, prevalence, and mortality of localized scleroderma in Quebec, Canada: a population-based study
Incidence, prevalence, and mortality of localized scleroderma in Quebec, Canada: a population-based study Open
This project was funded by Canadian Dermatology Foundation, National Scleroderma Foundation and Canadian Institutes of Health Research. Dr. Netchiporouk received FRQS Junior 1 Clinician Scientist Salary Award.
View article: Morphea, Eosinophilic Fasciitis and Cancer: A Scoping Review
Morphea, Eosinophilic Fasciitis and Cancer: A Scoping Review Open
Morphea is an autoimmune fibrotic skin disease. Eosinophilic fasciitis (EF) is considered to belong to the severe spectrum of morphea. We conducted a scoping review assessing the risk of secondary cancer among morphea/EF patients, paraneop…
View article: Accurate diagnosis of acute hemorrhagic edema of infancy: a French multicenter observational study
Accurate diagnosis of acute hemorrhagic edema of infancy: a French multicenter observational study Open
View article: Importance of predicting non-response to intravenous immunoglobulin therapy in non-Asian patients with Kawasaki disease
Importance of predicting non-response to intravenous immunoglobulin therapy in non-Asian patients with Kawasaki disease Open
View article: Use of the Auto-inflammatory Disease Activity Index to monitor disease activity in patients with colchicine-resistant Familial Mediterranean Fever, Mevalonate Kinase Deficiency, and TRAPS treated with canakinumab
Use of the Auto-inflammatory Disease Activity Index to monitor disease activity in patients with colchicine-resistant Familial Mediterranean Fever, Mevalonate Kinase Deficiency, and TRAPS treated with canakinumab Open
The AIDAI allows to discriminate between patients with active and inactive HRFs, and can be used in clinical practice to monitor the disease course of patients and the effect of medications.
View article: Plasma exchange and glucocorticoid dosing for patients with ANCA-associated vasculitis: a clinical practice guideline
Plasma exchange and glucocorticoid dosing for patients with ANCA-associated vasculitis: a clinical practice guideline Open
Clinical questions What is the role of plasma exchange and what is the optimal dose of glucocorticoids in the first 6 months of therapy of patients with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV)? This guideline…
View article: Epidemiology of Kawasaki Disease in Europe
Epidemiology of Kawasaki Disease in Europe Open
Aim of the review: To review major epidemiological aspects of Kawasaki disease (KD) in Europe, describing demographic characteristics, revising its incidence along with time trends and geographic variations, and describing migration studie…
View article: French recommendations for the management of Behçet’s disease
French recommendations for the management of Behçet’s disease Open
View article: Acute acral eruptions in children during the COVID-19 pandemic: Characteristics of 103 children and their family clusters
Acute acral eruptions in children during the COVID-19 pandemic: Characteristics of 103 children and their family clusters Open
View article: Delineating phenotypes of Kawasaki disease and SARS-CoV-2-related inflammatory multisystem syndrome: a French study and literature review
Delineating phenotypes of Kawasaki disease and SARS-CoV-2-related inflammatory multisystem syndrome: a French study and literature review Open
Objective To better define the clinical distinctions between the new severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2)-related paediatric inflammatory multisystem syndrome (PIMS) and Kawasaki disease (KD). Methods We compared th…
View article: Phenotypic Associations of PSTPIP1 Sequence Variants in PSTPIP1-Associated Autoinflammatory Diseases
Phenotypic Associations of PSTPIP1 Sequence Variants in PSTPIP1-Associated Autoinflammatory Diseases Open
View article: Missed or delayed diagnosis of Kawasaki disease during the 2019 novel coronavirus disease (COVID-19) pandemic
Missed or delayed diagnosis of Kawasaki disease during the 2019 novel coronavirus disease (COVID-19) pandemic Open
View article: Defining the risk of first intravenous immunoglobulin unresponsiveness in non-Asian patients with Kawasaki disease
Defining the risk of first intravenous immunoglobulin unresponsiveness in non-Asian patients with Kawasaki disease Open
View article: Contribution of rare and predicted pathogenic gene variants to childhood-onset lupus: a large, genetic panel analysis of British and French cohorts
Contribution of rare and predicted pathogenic gene variants to childhood-onset lupus: a large, genetic panel analysis of British and French cohorts Open
View article: Linear cutaneous lupus erythematosus in children—report of two cases and review of the literature: A case report
Linear cutaneous lupus erythematosus in children—report of two cases and review of the literature: A case report Open
Linear cutaneous lupus erythematosus is an unusual presentation of cutaneous lupus following Blaschko’s lines. It is described mostly in children and young adults and is usually not associated with systemic involvement. We report two cases…
View article: Limites nosologiques entre fièvre méditerranéenne familiale et spondylarthrite juvénile : analyse de trois cohortes rétrospectives françaises
Limites nosologiques entre fièvre méditerranéenne familiale et spondylarthrite juvénile : analyse de trois cohortes rétrospectives françaises Open
View article: Clinical Profile of Methotrexate-resistant Juvenile Localised Scleroderma
Clinical Profile of Methotrexate-resistant Juvenile Localised Scleroderma Open
Methotrexate has demonstrated its efficiency for the treatment of juvenile localized scleroderma but some patients may be resistant. The aim of our study was to define the profile of such patients. We performed an observational retrospecti…
View article: Vaccination and Risk of Childhood IgA Vasculitis
Vaccination and Risk of Childhood IgA Vasculitis Open
BACKGROUND AND OBJECTIVES: Immunoglobulin A vasculitis (IgAV) might develop after vaccination. However, this potential relationship is essentially based on case reports, and robust pharmaco-epidemiologic data are scarce. We aimed to invest…
View article: Health-related quality of life in children with PFAPA syndrome
Health-related quality of life in children with PFAPA syndrome Open
View article: The use of interleukin 1 receptor antagonist (anakinra) in Kawasaki disease: A retrospective cases series
The use of interleukin 1 receptor antagonist (anakinra) in Kawasaki disease: A retrospective cases series Open
View article: Standard dose of Ustekinumab for childhood-onset deficiency of interleukin–36 receptor antagonist
Standard dose of Ustekinumab for childhood-onset deficiency of interleukin–36 receptor antagonist Open
View article: Value of biomarkers for predicting immunoglobulin A vasculitis nephritis outcome in an adult prospective cohort
Value of biomarkers for predicting immunoglobulin A vasculitis nephritis outcome in an adult prospective cohort Open
Background Henoch–Schönlein purpura, more recently renamed immunoglobulin A vasculitis (IgAV), is a systemic vasculitis characterized by IgA deposits. The current markers used to assess IgAV inaccurately evaluate the risk of nephritis occu…
View article: THU0509 Improvement of disease activity in patients with colchicine-resistant FMF, HIDS/MKD and traps assessed by autoinflammatory disease activity index (AIDAI): results from the cluster trial
THU0509 Improvement of disease activity in patients with colchicine-resistant FMF, HIDS/MKD and traps assessed by autoinflammatory disease activity index (AIDAI): results from the cluster trial Open
View article: Incidence of IgA vasculitis in children estimated by four-source capture–recapture analysis: a population-based study
Incidence of IgA vasculitis in children estimated by four-source capture–recapture analysis: a population-based study Open
Our study supports secular and geospatial stability in childhood IgAV incidence and adds further indirect evidence for a possible role of a ubiquitous, non-emerging infectious trigger. Incidence studies from understudied areas are needed t…
View article: Kawasaki disease in adults: Observations in France and literature review
Kawasaki disease in adults: Observations in France and literature review Open