Prune belly syndrome
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Congenital Disorders of the Human Urinary Tract: Recent Insights From Genetic and Molecular Studies Open
The urinary tract comprises the renal pelvis, the ureter, the urinary bladder, and the urethra. The tract acts as a functional unit, first propelling urine from the kidney to the bladder, then storing it at low pressure inside the bladder …
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Prune belly syndrome: current perspectives Open
Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often requi…
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Factors Associated With the Development of Chronic Kidney Disease in Children With Congenital Anomalies of the Kidney and Urinary Tract Open
Congenital anomalies of the kidney and urinary tract (CAKUT) are the most common cause of end-stage renal disease in children and adolescents. The diversity of the malformations summarized by CAKUT is high and there are numerous associated…
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Prune belly syndrome: Approaches to its diagnosis and management Open
Prune Belly syndrome (PBS) or Eagle-Barrett syndrome is an anatomo-radiological syndrome consisting of a complex and rare malformation characterized by the following triad of symptoms: deficiency of the abdominal muscles, malformations of …
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Prenatal imaging of genital defects: clinical spectrum and predictive factors for severe forms Open
Objectives To report the clinical spectrum of genital defects diagnosed before birth, identify predictive factors for severe phenotypes at birth, and determine the rate of associated malformations. Patients and methods A retrospective stud…
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Single-center outcome analysis of 46 fetuses with megacystis after intrauterine vesico-amniotic shunting with the Somatex®intrauterine shunt Open
Objectives To assess the spectrum of underlying pathologies, the intrauterine course and postnatal outcome of 46 fetuses with megacystis that underwent intrauterine vesico-amniotic shunting (VAS) with the Somatex® shunt in a single center.…
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Signs and symptoms of developmental abnormalities of the genitourinary tract Open
The suggestions shown here can help the pediatrician to establish clinical hypotheses for the early diagnosis of developmental abnormalities of the genitourinary tract without resorting to expensive and invasive procedures.
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Continuous Positive Airway Pressure Belly Syndrome: Challenges of a Changing Paradigm Open
In extreme preterm infants, early use of continuous positive airway pressure (CPAP) for respiratory support reduces the incidence of chronic lung disease. However, as a sequel, inadvertent passage of air into the gastrointestinal tract lea…
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Pseudo Prune Belly Syndrome: Diagnosis Revealed by Imaging – A Case Report and Brief Review Open
Background: Prune Belly Syndrome (PBS) is a rare entity, usually found in male neonates. It comprises complex urinary tract anomalies, bilateral undescended testis and absence of anterior abdominal wall muscles. Patients with unilateral ab…
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Prune belly syndrome, a rare case presentation in neonatology: about one case in Yaounde, Cameroon Open
The Prune-Belly syndrome (PBS) is a rare pathology predominating in male infants, classically manifesting with the triad including aplasia of the abdominal wall muscles, dilatation of the urinary tract, and testicular abnormalities. We rep…
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The role of intra-abdominal pressure in human testicular migration Open
Abdominal pressure wound is an auxiliary force in testicular migration. Patients with abdominal wall defects are associated with undescendend testis in more than 30% of the cases probably due to mechanical factors; the Prune Belly Syndrome…
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The incidence of apparent congenital urogenital anomalies in North Indian newborns: A study of 20,432 pregnancies Open
Introduction and objectives: Over the last few decades, congenital anomalies of the urogenital system have increased globally as a consequence of advanced maternal age at pregnancy and developments in assisted reproductive techniques. The …
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Prune belly syndrome: A report of 15 cases from Sudan. Open
Prune belly syndrome is a rare congenital malformation of unknown aetiology, composed of a triad of deficient abdominal wall muscle, cryptorchidism and urinary tract anomalies. The majority of patients have associated pulmonary, skeletal, …
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Study of Testicular Structure in Fetuses with Prune Belly Syndrome Open
Purpose . To compare the structure of the testis in fetuses with prune belly syndrome (PBS) to normal controls. Materials and Methods . We studied 6 testes obtained from 3 fetuses with PBS and 14 testes from 7 male fetuses. The testicular …
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Clinical, ultrasonographic, and postmortem findings in sheep and goats with urinary tract disorders Open
Background and Aim: In sheep and goats, most urinary disorders are incidental findings at the postmortem examination and do not present clinically. As such, the diagnosis of renal diseases in sheep and goats can be overlooked. Therefore, t…
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Vesicoamniotic Shunting Improves Outcomes in a Subset of Prune Belly Syndrome Patients at a Single Tertiary Center Open
[This corrects the article DOI: 10.3389/fped.2018.00180.].
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Challenging diagnosis of prune belly syndrome antenatally: a case report Open
We conclude that suspicion of such anomalies through an early antenatal scan require an urgent further follow-up scan in a tertiary center. The referral to the tertiary center must be to an experienced ultrasonographer and maternal-fetal m…
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Three cases of prune belly syndrome at the Lagos State University Teaching Hospital, Ikeja Open
Prune belly syndrome (PBS) is a rare congenital disorder affecting 2.5 to 3.8/100,000 live births worldwide. Our objective of this report is to describe clinical manifestation, laboratory, and radiological characteristics of PBS in our pat…
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Quadratus lumborum block for post-operative pain relief in patient with Prune belly syndrome Open
Abdominal field blocks are commonly used as part of multimodal analgesia for post-operative pain relief in patients undergoing abdominal surgery. Conventionally, transversus abdominis plane block is used, but has the disadvantage of limite…
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Dental treatment of patients with prune belly syndrome Open
Background Prune belly syndrome (PBS), also known as Eagle‐Barrett syndrome (EGBRS), is a rare congenital disease characterized by deficiency or absence of abdominal wall muscles, urological abnormalities, and bilateral cryptorchidism. Typ…
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Prune belly syndrome: current perspectives Open
Angela M Arlen,1 Cayce Nawaf,1 Andrew J Kirsch21Yale University School of Medicine, Department of Urology, New Haven, CT 06520, USA; 2Emory University, Childrens Healthcare of Atlanta, Atlanta, GA 30328, USAAbstract: Prune belly syndrome (…
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An autopsy case report: prune belly syndrome with overlapping presentation of partial urorectal septum malformation sequence Open
Prune belly syndrome (PBS) is characterized by a classical triad of congenitally absent abdominal muscles, bilateral cryptorchidism, and a malformed urinary tract. Urorectal septum malformation sequence (URSM) is identified with the absenc…
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Renal complication due to prune belly syndrome: A case report Open
Introduction: Prune belly syndrome (PBS) is a congenital disorder characterized by injury or hypoplasia of the abdominal wall musculature, severe urinary tract abnormalities, and bilateral cryptorchidism in males. It has an estimated incid…
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It’s not All Doom and Gloom: Prune Belly Syndrome Associated with VACTERL Open
Prune belly syndrome is a rare abnormality; its association with VACTERL is even rarer. This association has been reported in literature a few times since first reported in 1993 and so far the majority have either been stillbirths or died …
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A novel technique of abdominoplasty for prune belly syndrome Open
Prune belly syndrome is an extremely rare congenital condition occurring predominantly in males. This triad syndrome comprises of partial or complete deficient abdominal wall muscles, undescended testes and dilated urinary collecting syste…
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Megacystis microcolon intestinal hypoperistalsis syndrome overlapping prune belly syndrome Open
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital visceral myopathy. We experienced a case of an infant with MMIHS with prune belly syndrome (PBS). A pregnant woman was transferred at 16 gestational wee…
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The challenging diagnosis and management of the prune belly syndrome: A case report Open
Prune belly syndrome is a rare disorder that occurs mainly in men. It is characterized by the triad of deficient abdominal wall muscles, the dilated urinary collecting system, bilateral cryptorchidism, and infertility. It mainly affects th…
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Prune belly syndrome: A rare case report Open
Key Clinical Message In babies presenting with an omphalocele, other components of the prune belly syndrome should be scrutinized for early diagnosis and timely intervention. Abstract A male baby on his 13th day of life presented with an o…
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Prune Belly Syndrome: A Ten-Year Single Tertiary Centre Experience in South-South, Nigeria Open
Background: Prune belly syndrome (PBS) is a congenital anomaly that consists of a triad of abdominal wall defect, bilateral cryptorchidism, and urinary tract dilation. The disease is of varying severity. This study aims to highlight the ch…
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Unusual variant of pseudo prune belly syndrome Open
Unilateral pseudo prune belly syndrome (PPBS) is a rare variant with only two other cases found in the main literature until. We present a 9-month old boy with left-sided lax abdominal wall, undescended testes and major vesicoureteric refl…